Modern terminology for Frontotemporal Dementia (FTD) has been expanding. Now, FTD is included within a larger group of neurodegenerative conditions including Progressive Supranuclear Palsy (PSP), Corticobasal Degeneration (CBD), FTD with Parkinsonism, and FTD with Atrophic Lateral Sclerosis (ALS). The combined set of diseases including FTD behavioral variant and PPA is referred to as Frontotemporal Lobar Degeneration (or Dementia).

At the present time, a variety of factors (including the research literature, the interests of advocacy groups for individual diseases, and prior medical practices) continue to the nomenclature and typology of these diseases inconsistent in different places.